Infantile hypertrophic cardiomyopathy with QT prolongation.

Prevalence and clinical correlates of QT prolongation in patients with hypertrophic cardiomyopathy.

AIMS Congenital or acquired QT prolongation is a risk factor for life-threatening arrhythmias. In patients with hypertrophic cardiomyopathy (HCM), the QT interval may be intrinsically prolonged. However, the prevalence, cause, and significance of QT prolongation among patients with HCM are unknown. METHODS AND RESULTS After exclusion of patients on QT-prolonging drugs, a blinded, retrospectiv...

Multifactorial QT Interval Prolongation and Takotsubo Cardiomyopathy

A 71-year-old woman collapsed while working as a grocery store cashier. CPR was performed and an AED revealed torsades de pointes (TdP). She was subsequently defibrillated resulting in restoration of sinus rhythm with a QTc interval of 544 msec. Further evaluation revealed a diagnosis of Takotsubo Cardiomyopathy (TCM) contributing to the development of a multifactorial acquired long QT syndrome...

Torsades de Pointes in Takotsubo Cardiomyopathy with QT Prolongation

Takotsubo cardiomyopathy, or stress-induced cardiomyopathy, is characterized by reversible left ventricular apical ballooning associated with emotional or physiologic stress, mimicking acute myocardial infarction in the absence of significant coronary artery disease at angiography. Although the prognosis for patients with Takotsubo cardiomyopathy is relatively good, it is reported to be associa...

DIFFUSE CORONARY ARTERIAL ECTASIA WITH HYPERTROPHIC CARDIOMYOPATHY

A 40 year old male, a known case of hypertrophic cardiomyopathy, was admitted for catheterization. At catheterization and angiography, septum was hypertrophied to about 5cm and diffuse coronary artery aneurysm was revealed. We found no previous report of coronary artery aneurysm in hypertrophic cardiomyopathy.

Atypical Infantile-onset Pompe Disease with Hypertrophic Cardiomyopathy